Синдром Чедиака-Хигаси (обзор литературы и собственные клинические наблюдения)
https://doi.org/10.24287/1726-1708-2016-15-1-27-33
Аннотация
Ключевые слова
дети,
первичный иммунодефицит,
синдром Чедиака-Хигаси,
глазо-кожный альбинизм,
гигантские пероксидазаположительные гранулы,
первичный гемофагоцитарный лимфогистиоцитоз,
трансплантация гемопоэтических стволовых клеток,
режим кондиционирования со сниженной интенсивностью,
children,
primary immunodeficiency,
Chediak-Higashi syndrome,
oculocutaneous albinism,
peroxidase-positive giant granules,
primary hemophagocytic lymphohistiocytosis,
hematopoietic stem cell transplantation,
reduced intensity conditioning
Об авторах
Юлия Александровна Родина
Федеральный научно-клинический центр детской гематологии, онкологии и иммунологии им. Дмитрия Рогачева Минздрава России
Россия
Россия
Виктор Евгеньевич Матвеев
Федеральный научно-клинический центр детской гематологии, онкологии и иммунологии им. Дмитрия Рогачева Минздрава России
Россия
Россия
Дмитрий Николаевич Балашов
Федеральный научно-клинический центр детской гематологии, онкологии и иммунологии им. Дмитрия Рогачева Минздрава России
Россия
Россия
Мария Эдуардовна Дубровина
Федеральный научно-клинический центр детской гематологии, онкологии и иммунологии им. Дмитрия Рогачева Минздрава России
Россия
Россия
Анна Юрьевна Щербина
Федеральный научно-клинический центр детской гематологии, онкологии и иммунологии им. Дмитрия Рогачева Минздрава России
Россия
Россия
Список литературы
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Рецензия
Для цитирования:
Родина Ю.А., Матвеев В.Е., Балашов Д.Н., Дубровина М.Э., Щербина А.Ю. Синдром Чедиака-Хигаси (обзор литературы и собственные клинические наблюдения). Вопросы гематологии/онкологии и иммунопатологии в педиатрии. 2016;15(1):27-33. https://doi.org/10.24287/1726-1708-2016-15-1-27-33
For citation:
Rodina Yu.A., Matveev V.E., Balashov D.N., Dubrovina M.E., Shcherbina A.Yu. Chediak-Higashi syndrome (Review of literature and clinical case reports). Pediatric Hematology/Oncology and Immunopathology. 2016;15(1):27-33. (In Russ.) https://doi.org/10.24287/1726-1708-2016-15-1-27-33
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