Опыт ведения больных с гипep-IgD-синдромом (синдромом дефицита мевалонаткиназы)
https://doi.org/10.24287/1726-1708-2016-15-1-46-53
Аннотация
Ключевые слова
дети,
аутовоспалительные заболевания,
периодические синдромы,
гипер-IgD-синдром,
мевалонаткиназа,
мевалоновая ацидурия,
ингибиторы интерлейкина-1,
children,
autoinflammatory diseases,
periodic fever syndromes,
hyper-IgD syndrome,
mevalonate kinase,
mevalonic aciduria,
interleukin-1 inhibitors
Об авторах
Анна Леонидовна Козлова
Федеральный научно-клинический центр детской гематологии, онкологии и иммунологии им. Дмитрия Рогачева, Минздрава России
Россия
Россия
Татьяна Владимировна Варламова
Федеральный научно-клинический центр детской гематологии, онкологии и иммунологии им. Дмитрия Рогачева, Минздрава России
Россия
Россия
Сергей Борисович Зимин
Детская городская клиническая больница № 9 им. Г.Н. Сперанского Департамента здравоохранения Москвы
Россия
Россия
Галина Анатольевна Новичкова
Федеральный научно-клинический центр детской гематологии, онкологии и иммунологии им. Дмитрия Рогачева, Минздрава России
Россия
Россия
Анна Юрьевна Щербина
Федеральный научно-клинический центр детской гематологии, онкологии и иммунологии им. Дмитрия Рогачева, Минздрава России
Россия
Россия
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Рецензия
Для цитирования:
Козлова А.Л., Варламова Т.В., Зимин С.Б., Новичкова Г.А., Щербина А.Ю. Опыт ведения больных с гипep-IgD-синдромом (синдромом дефицита мевалонаткиназы). Вопросы гематологии/онкологии и иммунопатологии в педиатрии. 2016;15(1):46-53. https://doi.org/10.24287/1726-1708-2016-15-1-46-53
For citation:
Kozlova A.L., Varlamova T.V., Zimin S.B., Novichkova G.A., Shcherbina A.Yu. Experience gained in the treatment of patients with hyper-IgD syndrome (mevalonate kinase deficiency). Pediatric Hematology/Oncology and Immunopathology. 2016;15(1):46-53. (In Russ.) https://doi.org/10.24287/1726-1708-2016-15-1-46-53
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