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Вопросы гематологии/онкологии и иммунопатологии в педиатрии

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Description of health related quality of life of children and adolescents with hemophilia from India

https://doi.org/10.24287/1726-1708-2020-19-3-12-16

Полный текст:

Аннотация

Hemophilia is a genetic disease that impairs quality of life due to its chronicity of nature where the individual will experience spontaneous bleeding or bleeding after an injury which requires frequent visits to the hospital for treatment. The objective of this study was to find the Health-related quality of life (HRQoL) of children and adolescents with moderate and severe hemophilia between 6 years and 16 years using the Haemo-QoL questionnaire. A prospective survey was carried out among 107 children and adolescents from two hemophilia treatment centers in Karnataka state. Approval was taken from the ethical committee. The data was analyzed using SPSS version 16.0. The mean age was 11.00 ± 2.98 years. Among the 107 participants, 89.70% had hemophilia A and 10.30% had hemophilia B. Moderate hemophilia was found among 54.20% participants and 45.80% had severe hemophilia. Overall, the HRQoL scores (55.41) were higher in the age group of 6–7 years compared to 8–12 years and 13–16 years. The mean HRQoL in the domain of family were: 77.84 ± 23.12 among 6–7 years, 66.00 ± 17.34 among the 8–12 years and 60.38 ± 16.72 among 13–16 years. Children demonstrated poor HRQoL in the domains of family and friends. The results indicate a need for continuous monitoring of QoL to identify better treatment methods.

Об авторах

A. Dsouza
Manipal College of Nursing Manipal Academy of Higher Education
Индия
Manipal


D. Nayak
TMA Pai Hospital, Udupi, Manipal Melaka Medical College, Manipal Academy of Higher Education
Индия
Manipal


A. Kurien
Manipal Melaka Medical College, Academy of Higher Education
Индия
Manipal


M. S. Pai
Manipal Academy of Higher Education
Индия
Manipal


B. S. Nayak
Manipal College of Nursing Manipal Academy of Higher Education
Индия
Manipal


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Для цитирования:


Dsouza A., Nayak D., Kurien A., Pai M.S., Nayak B.S. Description of health related quality of life of children and adolescents with hemophilia from India. Вопросы гематологии/онкологии и иммунопатологии в педиатрии. 2020;19(3):12-16. https://doi.org/10.24287/1726-1708-2020-19-3-12-16

For citation:


Dsouza A., Nayak D., Kurien A., Pai M.S., Nayak B.S. Description of health related quality of life of children and adolescents with hemophilia from India. Pediatric Hematology/Oncology and Immunopathology. 2020;19(3):12-16. https://doi.org/10.24287/1726-1708-2020-19-3-12-16

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ISSN 1726-1708 (Print)
ISSN 2414-9314 (Online)